Chiari II malformation

Case contributed by Dr Amr Farouk

Presentation

1-month-old neonate presenting with myelomeningocele for CNS survey.

Patient Data

Age: 1 month old
Gender: Female
MRI

Infra-tentorial findings:

  • Crowded foramen magnum with the cerebellar tonsils and vermis seen displaced inferiorly.
  • Small posterior fossa with a low attachment of the tentorium and low torcula.
  • Pulled down brainstem with an elongated and low lying fourth ventricle.
  • Tectal plate beaking.
  • Angulation of the aqueduct.
  • Concavity of clivus

Supratentorial findings:

Case Discussion

The constellation of the supra and infra-tentorial CNS findings in addition to the myelomeningocele are of a Chiari II malformation.

PlayAdd to Share

Case information

rID: 58484
Published: 19th Feb 2018
Last edited: 16th Jul 2018
Inclusion in quiz mode: Included
Institution: National cancer institute, Cairo, Egypt

Updating… Please wait.
Loadinganimation

Alert accept

Error Unable to process the form. Check for errors and try again.

Alert accept Thank you for updating your details.